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food for special medical purposes for use in the dietary management of Homocystinuira
- from 4 months to 6 years
- highly concentrated protein supplement free from methionine (Met) - in powder form
- cystin-enriched
- low calorie: no carbohydrate, no fat
- neutral, characteristic taste
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highly purified L-amino acids
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micronutrients in adequate amounts
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available in a 500 g tin or in convenient portion sachets at 5 g protein equivalent
Dosage and use
The total daily amount of a protein supplement depends on age, body weight and individual metabolic status and is determined under medical supervision. The daily quantity of the protein supplement should be taken in 3 - 5 single portions during the day. The daily dose of amino acid mixture may consist either exclusively of ZeroMet K or of a combination of several amino acid mixtures suitable for the dietary management of Homocystinuria. The diet must be supplemented with energy, natural protein and other nutrients.
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Average content:
Amino acid profile per 100 g powder
| L-Amino acid |
per 100 g |
L-Amino acid |
per 100 g |
| L-Alanine |
4,7 g |
L-Leucine |
6,6 g |
| L-Arginine |
3,6 g |
L-Lysine |
5,2 g |
| L-Aspartic acid |
11,3 g |
L-Phenylalanine |
3,1 g |
| L-Cystine |
3,3 g |
L-Proline |
8,6 g |
| L-Glutamic acid |
7,8 g |
L-Serine |
4,5 g |
| L-Glutamine |
2,1 g |
L-Threonine |
4,7 g |
| Glycine |
5,0 g |
L-Tryptophan |
1,5 g |
| L-Histidine |
1,7 g |
L-Tyrosine |
3,6 g |
| L-Isoleucine |
4,2 g |
L-Valine |
5,8 g |
Nutrition information
| Nutrient |
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Powder |
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100 g |
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| Energy |
kJ |
1240 |
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kcal |
292 |
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| Protein* |
g |
72 |
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| Amino acids |
g |
87 |
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| (*Converison: 1 g protein equivalent to 1,2 g amino acids) |
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| Carbohydrates |
g |
0 |
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| Fat |
g |
0 |
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100 g |
g protein |
| Minerals |
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| Sodium |
mg |
1050 |
14 |
| Potassium |
mg |
1857 |
26 |
| Calcium |
mg |
2228 |
31 |
| Magnesium |
mg |
334 |
4,6 |
| Phosphorus |
mg |
1188 |
16 |
| Chloride |
mg |
637 |
8,7 |
| Iron |
mg |
33 |
0,45 |
| Trace elemens |
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| Zinc |
mg |
27 |
0,37 |
| Copper |
mg |
2,9 |
0,04 |
| Iodine |
µg |
386 |
5,3 |
| Manganese |
mg |
5,9 |
0,08 |
| Chromium |
µg |
156 |
2,1 |
| Fluoride |
µg |
1114 |
15,3 |
| Molybdenum |
µg |
117 |
1,6 |
| Selenium |
µg |
54 |
0,7 |
| Vitamins |
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| Vitamin A |
mg |
2,2 |
0,03 |
| Vitamin D3 |
µg |
12 |
0,16 |
| Vitamin E |
mg |
26 |
0,36 |
| Vitamin K1 |
µg |
67 |
0,9 |
| Vitamin B1 |
mg |
2,6 |
0,036 |
| Vitamin B2 |
mg |
3,3 |
0,045 |
| Vitamin B6 |
mg |
3,3 |
0,045 |
| Vitamin C |
mg |
120 |
1,6 |
| Niacin |
mg |
33 |
0,45 |
| Biotin |
µg |
297 |
4,1 |
| Folic acid |
µg |
557 |
7,6 |
| Vitamin B12 |
µg |
6,7 |
0,09 |
| Pantothenic acid |
mg |
14,9 |
0,2 |
| Carnitine |
mg |
67 |
0,9 |
| Taurine |
mg |
74 |
1,0 |
| Choline |
mg |
297 |
4,1 |
| myo-Inositol |
mg |
349 |
4,8 |
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