{"id":19496,"date":"2024-09-23T10:58:39","date_gmt":"2024-09-23T08:58:39","guid":{"rendered":"https:\/\/metax.org\/methylmalonic-aciduria-propionic-aciduria-mma-pa\/leucine\/"},"modified":"2026-02-06T09:27:23","modified_gmt":"2026-02-06T08:27:23","slug":"leucine","status":"publish","type":"page","link":"https:\/\/metax.org\/en\/methylmalonic-aciduria-propionic-aciduria-mma-pa\/leucine\/","title":{"rendered":"Leucin"},"content":{"rendered":"<p><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-sizes-top:0px;--awb-border-sizes-bottom:0px;--awb-border-sizes-left:0px;--awb-border-sizes-right:0px;--awb-border-color:var(--awb-custom_color_2);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-bottom:0px;--awb-padding-left:0px;--awb-margin-top:48px;--awb-margin-bottom:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-center fusion-flex-align-content-flex-start fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-padding-top:20px;--awb-padding-right:23px;--awb-padding-bottom:12px;--awb-padding-left:20px;--awb-bg-image:radial-gradient(circle at center center, var(--awb-color1) 0%,rgba(228,212,87,0.37) 100%);--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:2.016%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:2.016%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:2.016%;--awb-spacing-left-medium:2.016%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-image-element \" style=\"text-align:center;--awb-max-width:500px;--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-1 hover-type-none\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" title=\"Leucin can\" src=\"https:\/\/metax.org\/wp-content\/uploads\/de_ds_leucin.png\" alt class=\"img-responsive wp-image-19497\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/de_ds_leucin-200x126.png 200w, https:\/\/metax.org\/wp-content\/uploads\/de_ds_leucin-400x252.png 400w, https:\/\/metax.org\/wp-content\/uploads\/de_ds_leucin.png 540w\" sizes=\"auto, (max-width: 640px) 100vw, 540px\" \/><\/span><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-2 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-sizes-bottom:0px;--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-right:40px;--awb-padding-bottom:20px;--awb-padding-left:40px;--awb-padding-right-small:12px;--awb-padding-left-small:12px;--awb-margin-top:30px;--awb-margin-bottom:30px;--awb-background-color:var(--awb-color1);--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-padding-top:30px;--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-1\"><h1 class=\"\" style=\"text-align: center;\" data-fontsize=\"48\" data-lineheight=\"57.6px\">Leucin<\/h1>\n<h2 class=\"\" style=\"text-align: center;\" data-fontsize=\"30\" data-lineheight=\"36px\">single amino acid<\/h2>\n<\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_1 1_1 fusion-flex-column fusion-flex-align-self-flex-start difp-produktbeschreibung\" style=\"--awb-padding-right:43px;--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-row\"><div class=\"fusion-text fusion-text-2\"><p>Leucin is highly concentrated L-leucine in powder form.<\/p>\n<p>Food for Special Medical Purposes (FSMP) for use in the dietary management of rare metabolic disorders, e.g. Maple Syrup Disease (MSUD), Methylmalonic Mciduria (MMA), Propionic Aciduria (PA) or LARS2 Deficiency, when supplementation with L-leucine is indicated.<\/p>\n<\/div><div style=\"text-align:left;\"><a class=\"fusion-button button-flat fusion-button-default-size button-custom fusion-button-default button-1 fusion-button-default-span fusion-button-default-type\" style=\"--awb-margin-top:40px;--awb-padding-top:10px;--awb-padding-right:10px;--awb-padding-bottom:8px;--awb-padding-left:10px;--button_accent_color:var(--awb-color2);--button_border_color:var(--awb-color2);--button_accent_hover_color:var(--awb-color1);--button_border_hover_color:var(--awb-color1);--button_border_width-top:2px;--button_border_width-right:2px;--button_border_width-bottom:2px;--button_border_width-left:2px;--button-border-radius-top-left:5px;--button-border-radius-top-right:5px;--button-border-radius-bottom-right:5px;--button-border-radius-bottom-left:5px;--button_gradient_top_color:rgba(255,255,255,0);--button_gradient_bottom_color:rgba(255,255,255,0);--button_gradient_top_color_hover:var(--awb-color3);--button_gradient_bottom_color_hover:var(--awb-color3);--button_font_size:18px;\" target=\"_blank\" rel=\"noopener noreferrer\" href=\"https:\/\/metax-tester.de\/produkt\/leucin-einzel-aminosaeure-2\/\"><span class=\"fusion-button-text awb-button__text awb-button__text--default\">Order Product Sample<\/span><\/a><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_1 1_1 fusion-flex-column fusion-flex-align-self-flex-start\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:28px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-block\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:20px;width:100%;\"><div class=\"fusion-separator-border sep-single sep-solid\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:#eaeaea;border-color:#eaeaea;border-top-width:1px;\"><\/div><\/div><div class=\"accordian fusion-accordian\" style=\"--awb-border-size:1px;--awb-icon-size:16px;--awb-content-font-size:var(--awb-typography4-font-size);--awb-icon-alignment:right;--awb-hover-color:var(--awb-color2);--awb-border-color:var(--awb-color3);--awb-background-color:var(--awb-color1);--awb-divider-color:var(--awb-color2);--awb-divider-hover-color:var(--awb-color3);--awb-icon-color:var(--awb-color1);--awb-title-color:var(--awb-color2);--awb-content-color:var(--awb-custom_color_3);--awb-icon-box-color:var(--awb-color2);--awb-toggle-hover-accent-color:var(--awb-color3);--awb-title-font-family:var(--awb-typography1-font-family);--awb-title-font-weight:var(--awb-typography1-font-weight);--awb-title-font-style:var(--awb-typography1-font-style);--awb-title-font-size:20px;--awb-content-font-family:var(--awb-typography4-font-family);--awb-content-font-weight:var(--awb-typography4-font-weight);--awb-content-font-style:var(--awb-typography4-font-style);\"><div class=\"panel-group fusion-toggle-icon-right fusion-toggle-icon-boxed\" id=\"accordion-19496-1\"><div class=\"fusion-panel panel-default difp-produktinformation panel-39fbf871890d4c247 fusion-toggle-has-divider\" style=\"--awb-title-color:var(--awb-color2);--awb-content-color:var(--awb-custom_color_3);\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_39fbf871890d4c247\"><a aria-expanded=\"false\" aria-controls=\"39fbf871890d4c247\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#39fbf871890d4c247\" href=\"#39fbf871890d4c247\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Product Information<\/span><\/a><\/h3><\/div><div id=\"39fbf871890d4c247\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_39fbf871890d4c247\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Would you like a PDF of our product information? Click on the following link: <a href=\"https:\/\/metax.org\/wp-content\/uploads\/metax_de_pi_leucin.pdf\" target=\"_blank\" rel=\"noopener\"><strong>DOWNLOAD \u2193<\/strong><\/a><\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-fc13fb02cee238912 fusion-toggle-has-divider\" style=\"--awb-title-color:var(--awb-color2);--awb-content-color:var(--awb-custom_color_3);\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_fc13fb02cee238912\"><a aria-expanded=\"false\" aria-controls=\"fc13fb02cee238912\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#fc13fb02cee238912\" href=\"#fc13fb02cee238912\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Consumer Information<\/span><\/a><\/h3><\/div><div id=\"fc13fb02cee238912\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_fc13fb02cee238912\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Would you like a PDF of our consumer information? Click on the following link:\u00a0 \u00a0<a href=\"https:\/\/metax.org\/wp-content\/uploads\/metax_de_vi_leucin.pdf\" target=\"_blank\" rel=\"noopener\"><strong>DOWNLOAD \u2193<\/strong><\/a><\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-34b2b3eb1f8ed1fb7 fusion-toggle-has-divider\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_34b2b3eb1f8ed1fb7\"><a aria-expanded=\"false\" aria-controls=\"34b2b3eb1f8ed1fb7\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#34b2b3eb1f8ed1fb7\" href=\"#34b2b3eb1f8ed1fb7\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Product Features<\/span><\/a><\/h3><\/div><div id=\"34b2b3eb1f8ed1fb7\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_34b2b3eb1f8ed1fb7\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<ul>\n<li>L-leucine &#8211; in powder form<\/li>\n<li>suitable for tube feeding<\/li>\n<li>100 g tin<\/li>\n<\/ul>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-3fa333dd73e7c4889 fusion-toggle-has-divider\" style=\"--awb-title-color:var(--awb-color2);--awb-content-color:var(--awb-custom_color_3);\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_3fa333dd73e7c4889\"><a aria-expanded=\"false\" aria-controls=\"3fa333dd73e7c4889\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#3fa333dd73e7c4889\" href=\"#3fa333dd73e7c4889\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Dosage<\/span><\/a><\/h3><\/div><div id=\"3fa333dd73e7c4889\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_3fa333dd73e7c4889\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p><span style=\"color: var(--awb-content-color); font-family: var(--awb-content-font-family); font-size: var(--awb-content-font-size); font-style: var(--awb-content-font-style); font-weight: var(--awb-content-font-weight); letter-spacing: var(--awb-content-letter-spacing); text-transform: var(--awb-content-text-transform);\">The daily dose depends on age, body weight, and individual metabolism and, like the time of intake, is determined under medical supervision. The powder should be taken with other foods and, if necessary, in addition to the usual amino acid\/protein supplement.<\/span><span style=\"color: var(--awb-content-color); font-family: var(--awb-content-font-family); font-size: var(--awb-content-font-size); font-style: var(--awb-content-font-style); font-weight: var(--awb-content-font-weight); letter-spacing: var(--awb-content-letter-spacing); text-transform: var(--awb-content-text-transform);\"> Leucin can be combined well with <\/span><a style=\"font-family: var(--awb-content-font-family); font-size: var(--awb-content-font-size); font-style: var(--awb-content-font-style); font-weight: var(--awb-content-font-weight); letter-spacing: var(--awb-content-letter-spacing); text-transform: var(--awb-content-text-transform);\" href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/\">ZeroVIL<\/a><span style=\"color: var(--awb-content-color); font-family: var(--awb-content-font-family); font-size: var(--awb-content-font-size); font-style: var(--awb-content-font-style); font-weight: var(--awb-content-font-weight); letter-spacing: var(--awb-content-letter-spacing); text-transform: var(--awb-content-text-transform);\"> or <\/span><a style=\"font-family: var(--awb-content-font-family); font-size: var(--awb-content-font-size); font-style: var(--awb-content-font-style); font-weight: var(--awb-content-font-weight); letter-spacing: var(--awb-content-letter-spacing); text-transform: var(--awb-content-text-transform);\" href=\"https:\/\/metax.org\/en\/methylmalonic-aciduria-propionic-aciduria-mma-pa\/\/\">ZeroTVMI<\/a> products.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-8ba2c9354a0ac8da5 fusion-toggle-has-divider\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_8ba2c9354a0ac8da5\"><a aria-expanded=\"false\" aria-controls=\"8ba2c9354a0ac8da5\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#8ba2c9354a0ac8da5\" href=\"#8ba2c9354a0ac8da5\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Important Notice<\/span><\/a><\/h3><\/div><div id=\"8ba2c9354a0ac8da5\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_8ba2c9354a0ac8da5\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Must only be used under medical supervision. Not for use as a sole source of nutrition. For enteral use only. Only for people with rare metabolic disorders, e.g. MSUD, MMA, PA or LARS2 Deficiency. Leucin is not suitable for infants in the first year of life.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-f9f2eb2bcf2c1bff3 fusion-toggle-has-divider\" style=\"--awb-content-font-size:20px;--awb-title-color:var(--awb-color2);--awb-content-color:var(--awb-custom_color_3);\"><div class=\"panel-heading\"><h3 class=\"panel-title toggle\" id=\"toggle_f9f2eb2bcf2c1bff3\"><a aria-expanded=\"false\" aria-controls=\"f9f2eb2bcf2c1bff3\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-19496-1\" data-target=\"#f9f2eb2bcf2c1bff3\" href=\"#f9f2eb2bcf2c1bff3\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon fa-arrow-circle-up fas\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon fa-arrow-circle-down fas\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Ordering Information<\/span><\/a><\/h3><\/div><div id=\"f9f2eb2bcf2c1bff3\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_f9f2eb2bcf2c1bff3\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<table border=\"1\" width=\"100%\">\n<tbody>\n<tr>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Product<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Packing<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Delivery Unit<\/h4>\n<\/td>\n<td style=\"text-align: center;\">\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"--fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">PZN (DE)<\/h4>\n<\/td>\n<td style=\"text-align: center;\">\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"--fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">PZN (AT)<\/h4>\n<\/td>\n<\/tr>\n<tr>\n<td><strong>Leucin<br \/>\n<\/strong><\/td>\n<td>tin \u00e0 100 g<\/td>\n<td>1 x 100 g<\/td>\n<td>19375659<\/td>\n<td>5863964<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/div><\/div><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-4 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:60px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-center fusion-title-text fusion-title-size-three\" style=\"--awb-margin-top-small:10px;--awb-margin-right-small:0px;--awb-margin-bottom-small:10px;--awb-margin-left-small:0px;\"><h3 class=\"fusion-title-heading title-heading-center fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:24;--minFontSize:24;line-height:var(--awb-typography1-line-height);\">Other products for MMA, PA and MSUD<\/h3><\/div><div class=\"fusion-image-carousel fusion-image-carousel-auto fusion-image-carousel-1 awb-image-carousel-top-below-caption\"><div class=\"awb-carousel awb-swiper awb-swiper-carousel awb-carousel--carousel awb-swiper-dots-position-bottom awb-imageframe-style awb-imageframe-style-below awb-imageframe-style-1\" data-layout=\"carousel\" data-autoplay=\"yes\" data-autoplayspeed=\"2500\" data-autoplaypause=\"no\" data-loop=\"yes\" data-columns=\"4\" data-columnsmedium=\"1\" data-columnssmall=\"1\" data-itemmargin=\"13\" data-itemwidth=\"180\" data-touchscroll=\"no\" data-freemode=\"no\" data-imagesize=\"auto\" data-scrollitems=\"1\" data-centeredslides=\"no\" data-rotationangle=\"50\" data-depth=\"100\" data-speed=\"500\" data-shadow=\"no\" data-pagination=\"bullets\" style=\"--awb-columns:4;\"><div class=\"swiper-wrapper awb-image-carousel-wrapper fusion-flex-align-items-center\"><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/valin100-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Valin100 minis, bei St\u00f6rungen im Aminos\u00e4urenstoffwechsel, z. B. Ahornsirupkrankheit (MSUD), Methylmalonacidurie (MMA) oder Propionacidurie (PA), wenn eine Erg\u00e4nzung mit L-Valin erforderlich ist, hochkonzentriertes, gepresstes und gecoatetes L-Valin in Tablettenform\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Valin100 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_minis_mit_verlauf_1.jpg\" class=\"attachment-full size-full\" alt=\"ZeroVIL minis\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_minis_mit_verlauf_1-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_minis_mit_verlauf_1-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_minis_mit_verlauf_1.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL minis<\/h3><p class=\"awb-imageframe-caption-text\">from 3 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/methylmalonazidurie-propionazidurie\/zerotvmi-k\/\" target=\"_self\"><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroTVMI K<\/h3><p class=\"awb-imageframe-caption-text\">4 months to 6 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/methylmalonazidurie-propionazidurie\/zerotvmi-j\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_j_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroTVMI J\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_j_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_j_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_j_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroTVMI J<\/h3><p class=\"awb-imageframe-caption-text\">7 to 14 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/methylmalonazidurie-propionazidurie\/zerotvmi-a\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroTVMI A\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroTVMI A<\/h3><p class=\"awb-imageframe-caption-text\">from 15 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/methylmalonazidurie-propionazidurie\/zerotvmi-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroTVMI minis\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_minis_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_minis_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_tvmi_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroTVMI minis<\/h3><p class=\"awb-imageframe-caption-text\">from 3 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/isoleucine100-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Isoleucin100 minis\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Isoleucin100 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-k\/\" target=\"_self\"><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL K<\/h3><p class=\"awb-imageframe-caption-text\">4 months to 6 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-j\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_j_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroVIL J\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_j_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_j_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_j_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL J<\/h3><p class=\"awb-imageframe-caption-text\">7 to 14 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-a\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_a_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroVIL A\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_a_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_a_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_a_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL A<\/h3><p class=\"awb-imageframe-caption-text\">from 15 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-smart-a\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_smart_a_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroVIL smart A\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_smart_a_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_smart_a_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_smart_a_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL smart A<\/h3><p class=\"awb-imageframe-caption-text\">from 15 years<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/metax_22329_de_ds_valin_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Valin, bei St\u00f6rungen im Aminos\u00e4urenstoffwechsel, z. B. Ahornsirupkrankheit (MSUD), Methylmalonacidurie (MMA) oder Propionacidurie (PA), wenn eine Erg\u00e4nzung mit L-Valin erforderlich ist, hochkonzentriertes L-Valin in Pulverform\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/metax_22329_de_ds_valin_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/metax_22329_de_ds_valin_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/metax_22329_de_ds_valin_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Valin<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/metax.org\/en\/maple-syrup-disease-msud\/zerovil-jump\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_jump_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"ZeroVIL jump\" srcset=\"https:\/\/metax.org\/wp-content\/uploads\/zero_vil_jump_mit_verlauf-200x126.jpg 200w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_jump_mit_verlauf-400x252.jpg 400w, https:\/\/metax.org\/wp-content\/uploads\/zero_vil_jump_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">ZeroVIL jump<\/h3><p class=\"awb-imageframe-caption-text\">from 3 years<\/p><\/div><\/div><\/div><\/div><\/div><div class=\"awb-swiper-button awb-swiper-button-prev\"><i class=\"awb-icon-angle-left\" aria-hidden=\"true\"><\/i><\/div><div class=\"awb-swiper-button awb-swiper-button-next\"><i class=\"awb-icon-angle-right\" aria-hidden=\"true\"><\/i><\/div><\/div><\/div><\/div><\/div><\/div><\/div><\/p>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":5,"featured_media":16049,"parent":18509,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-19496","page","type-page","status-publish","has-post-thumbnail","hentry"],"_links":{"self":[{"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/pages\/19496","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/users\/5"}],"replies":[{"embeddable":true,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/comments?post=19496"}],"version-history":[{"count":10,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/pages\/19496\/revisions"}],"predecessor-version":[{"id":22639,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/pages\/19496\/revisions\/22639"}],"up":[{"embeddable":true,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/pages\/18509"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/media\/16049"}],"wp:attachment":[{"href":"https:\/\/metax.org\/en\/wp-json\/wp\/v2\/media?parent=19496"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}