Single Amino Acids
All single amino acids are foods for special medical purposes. They are suitable for use in the dietary management of disorders in amino acid metabolism or other diseases requiring supplementation with the corresponding amino acid. The single amino acid supplements are highly concentrated and are available either in tablet form and/or in powder form. Especially the single amino acids in tablet form (minis) are odorless, tasteless and easy to swallow.
Product |
Dosage form |
Amino acid specification |
For dietary management of e.g. |
Download PDF |
Alanin | Powder | 100 g L-alanine/100 g | Glycogenosis (GSD) type II/Morbus Pompe | Download |
Arginin500 minis | Tablet form | 500 mg L-arginine/tablet | Urea Cycle Disorders | Download |
Citrullin500 minis | Tablet form | 500 mg L-citrulline/tablet | Urea Cycle Disorders | Download |
Citrullin | Powder | 100 g L-citrulline/100 g | Urea Cycle Disorders | Download |
Cystin | Powder | 100 g L-cystine/100 g | Homocystinuria | Download |
Glycin500 minis | Tablet form | 500 mg L-glycine/tablet | Isovaleric acidemia (IVA), serine deficiency diseases, creatine transporter defect (CRTR-D) | Download |
Glycin | Powder | 100 g L-glycine/100 g | Isovaleric acidemia (IVA), serine deficiency diseases, creatine transporter defect (CRTR-D) | Download |
Isoleucin100 minis | Tablet form | 100 mg L-isoleucine/tablet | MSUD, MMA, PA | Download |
Leucin | Powder | 100 g L-leucine/100 g | MSUD, MMA, PA | Download |
Lysine300 minis | Tablet form | 300 mg L-lysine/tablet | Hyperornithinemia-Hyperammonemia-Homocitrullinuria Syndrome (HHH), Lysinuric Protein Intolerance (LPI) | Download |
Magnesium L-aspartate | Powder | 69 g L-aspartic acid/100 g | mitochondrial aspartyl-trNA synthetase deficiency (DARS2 deficiency, LBSL) | Download |
Ornithin | Powder | 78 g L-ornithine/100 g | Arginase-1 Deficiency, GAMT Deficiency | Download |
Phenylalanin50 minis | Tablet form | 50 mg L-phenylalanine/tablet | Tyrosinemia, alkaptonuria, FARS2 defect | Download |
Phenylalanin | Powder | 100 g L-phenylalanine/100 g | Tyrosinemia, alkaptonuria, FARS2 defect | Download |
Serin500 minis | Tablet form | 500 mg L-serine/tablet | GRIN2B-associated encephalopathy or serine deficiency diseases | Download |
Serin | Powder | 100 g L-serine/100 g | GRIN2B-associated encephalopathy or serine deficiency diseases | Download |
Tryptophan | Powder | 100 g L-tryptophan/100 g | Pyridoxine-Dependent Epilepsy (PDE) | Download |
Tyrosin | Powder | 100 g L-tyrosine/100 g | PKU, HPA | Download |
Valin100 minis | Tablet form | 100 mg L-valine/tablet | MSUD, MMA, PA | Download |
Valin | Powder | 100 mg L-Valin/100 g | MSUD, MMA, PA | Download |